The objective of this paper is to report a case of extramammary Paget disease of the vulva, to describe its diagnosis, surgical\ntreatment, and outcome, and to discuss the general characteristics of this pathology. This is a rare neoplasm, found principally\nin areas in which apocrine and eccrine glands are numerous. This case report is relevant to the literature since the differential\ndiagnosis of extramammary Paget disease is difficult to be done only with the macroscopic appearance of the lesion and even\nwith the microscopic characteristics, requiring further studies, immunohistochemistry, as to differentiate pathologies. The present\nreport describes the case of a 63-year-old patient at the Santa Casa de Miseric�´ordia Hospital in Vit�´oria, Esp�´?rito Santo, Brazil, who\npresented with a hardened, ulcerated, and purplish lesion with hyperchromic and hypochromic spots, measuring 4 cm in diameter,\nlocated on the lower third of right labium majus, close to the vaginal fourchette. A right hemivulvectomy was performed, leaving\nwide margins all around.The patient progressed satisfactorily following surgery. Although extramammary Paget disease is rare, its\nincidence increases as a function of the patientâ��s age. Patients should be followed up closely because of the risk of persistence and/or\nrecurrence of the disease.
Loading....